Hyperimmunoglobulin E syndrome (Job's syndrome) in a-22-month old girl and IVIG treatment

Aka S., Sami Yazar A., CERAN Ö.

Marmara Medical Journal, cilt.16, sa.3, ss.207-210, 2003 (Scopus) identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 16 Sayı: 3
  • Basım Tarihi: 2003
  • Dergi Adı: Marmara Medical Journal
  • Derginin Tarandığı İndeksler: Scopus
  • Sayfa Sayıları: ss.207-210
  • Anahtar Kelimeler: Hyperimmunoglobulin E syndrome, Job's syndrome
  • İstanbul Medipol Üniversitesi Adresli: Evet

Özet

Hyperimmunoglobulin E syndrome is a rare disorder characterized by pruritic dermatitis, recurrent staphylococcal skin abscesses and extremely elevated concentrations of immunoglobulin E in serum. We report a patient who has pruritic vesiculopapules, recurrent episodes of skin abscesses on the scalp and face, and respiratory problems from the age of ten days (severe cough, wheezing, acute otitis media, pneumonia). She was diagnosed as Hyper-IgE syndrome and treated with IVIG along with antibiotics.