Hepatic epitheloid hemangioendothelioma: A rare indication for liver transplantation Hepatik epiteloid hemanjiyoendoteliyoma: Nadir bir karaciǧer nakli endikasyonu

Uraz S., Yaprak O., DAYANGAÇ M., Tokat Y.

Turkish Journal of Surgery, cilt.28, sa.1, ss.53-56, 2012 (Scopus) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 28 Sayı: 1
  • Basım Tarihi: 2012
  • Doi Numarası: 10.5097/1300-0705.ucd.808-11.01
  • Dergi Adı: Turkish Journal of Surgery
  • Derginin Tarandığı İndeksler: Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.53-56
  • Anahtar Kelimeler: Hepatic hemangioendothelioma, liver transplantation, liver tumor
  • İstanbul Medipol Üniversitesi Adresli: Evet

Özet

Hepatic epitheloid hemangioendothelioma: A rare indication for liver transplantation Hepatic epithelioid hemangioendothelioma is a rare malignancy arising from the vascular endothelial cells within the liver. The clinical manifestations are nonspecific, ranging from complete absence of symptoms to hepatic failure and death. Because the disease is rare, there is no clearly established therapeutic algorithm. Hepatic epithelioid hemangioendothelioma seems to be resistant to chemotherapy and radiotherapy. Either surgical resection or orthotopic liver transplantation is generally recommended as a curative treatment for this disease. However, in patients who have multifocal or diffuse enlargement, liver resection is frequently futile. We herein present a case with irresectable and metastatic hepatic hemangioendothelioma who underwent orthotopic liver transplantation and survived for 4 years.