Crouzon syndrome with multiple supernumerary teeth


Torun G., AKBULUT A.

Nigerian Journal of Clinical Practice, cilt.20, sa.2, ss.261-263, 2017 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 20 Sayı: 2
  • Basım Tarihi: 2017
  • Doi Numarası: 10.4103/1119-3077.187332
  • Dergi Adı: Nigerian Journal of Clinical Practice
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.261-263
  • Anahtar Kelimeler: Craniosynostosis, Crouzon syndrome, supernumerary teeth
  • İstanbul Medipol Üniversitesi Adresli: Evet

Özet

Crouzon syndrome (CS) is an autosomal dominant disorder characterized by craniofacial deformities caused by the early closure of cranial sutures. It is diagnosed by the presence of a flat sphenoid bone, protrusion of eyeballs (exophthalmos), and midfacial hypoplasia. Although hypodontia is usually present in cases with CS, supernumerary teeth are rarely seen. A 16-year-old male patient with CS was referred to our clinic. He had a high forehead, beaked nose, hypertelorism, palpebral ptosis, and asymmetrical orbits. Bilateral multiple supernumerary teeth were observed in his upper and lower jaws. Early diagnosis of CS is helpful in dental and craniofacial treatment. Because of multiple facial and oral problems, this patient required a multidisciplinary treatment approach.