Lhermitte-Duclos disease with orthostatic hypotension Ortostatik hipotansiyon ile birlikte izlenen Lhermitte-Duclos hastalığı olgusu

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HELVACI YILMAZ N., ŞEKER M., Omaygenç M. O., Yaka U., Eryiğit N., Yuluğ B.

Turk Noroloji Dergisi, vol.22, no.3, pp.130-132, 2016 (Scopus) identifier identifier

  • Publication Type: Article / Article
  • Volume: 22 Issue: 3
  • Publication Date: 2016
  • Doi Number: 10.4274/tnd.75428
  • Journal Name: Turk Noroloji Dergisi
  • Journal Indexes: Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.130-132
  • Keywords: Lhermitte-Duclos disease, orthostatic hypotension, cerebellum
  • Istanbul Medipol University Affiliated: Yes


Lhermitte-Duclos disease is a rare cerebellar dysplastic gangliocytoma. The most common symptoms include headache, nausea, vomiting, blurred vision, and imbalance. The typical appearance on cranial magnetic resonance imaging is hyper-intensity on T2-weighted images and hypo-intensity on T1-weighted images. The disease generally presents with benign progress. Development of obstructive hydrocephalus is an indication for urgent surgical intervention and surgery outcomes are satisfactory. Orthostatic hypotension is a very rare clinical presentation of this syndrome and ours is the second case of orthostatic hypotension to be reported in the literature.